Malformasi Anorektal. Anorectal malformations comprise a wide spectrum of diseases, which can affect boys and girls, and involve the distal anus and rectum as well as the urinary. Anorectal malformations (ARMs) are among the more frequent congenital anomalies encountered in paediatric surgery, with an estimated incidence ranging.

Author: Vudogrel Malasida
Country: India
Language: English (Spanish)
Genre: Career
Published (Last): 27 April 2004
Pages: 455
PDF File Size: 9.25 Mb
ePub File Size: 20.95 Mb
ISBN: 935-5-30241-789-6
Downloads: 59440
Price: Free* [*Free Regsitration Required]
Uploader: Zulugrel

Diagnostic methods The radiologic evaluation of a newborn with imperforate anus includes an abdominal ultrasound to evaluate for urologic anomalies. The presence of a single perineal orifice is clinical evidence of a patient with persistent cloaca. Voluntary muscle structures In the normal patient, the voluntary muscle structures are represented by the levators, muscle complex, and external sphincter.

For patients with a common channel greater than three cm, a laparotomy is usually required. There appears to be a low rate of association in families, but some appear to have an autosomal dominant inheritance pattern with a high incidence, as much as 1 in In the male, besides the absent anus, a note must be made of the anal pit. First; are there mwlformasi anomalies that threaten the baby’s life and should be dealt with right away?

Malformasi Anorektal | Lokananta | Jurnal Kedokteran Meditek

MRI is considered superior to CT scan because of excellent soft tissue characterization, multiplanar imaging, and lack of ionizing radiation. Often the vagina and urinary tract must be separated trying to gain length, and the urethra must then be reconstructed. Prospective long-term follow up of children with anorectal malformation: Various classifications have been proposed for CPC, but classification proposed by Rao et al.

This misconception has important therapeutic implications that will be discussed below.

These patients cannot have voluntary bowel movements and require an artificial mechanism to empty their colon, a daily enema. So Rehbein performed endorectal pull-through to avoid any damage to the pelvic innervations.

Male newborns with rectoperineal fistula do not need a colostomy. A more anorrktal assessment of the sacrum can be obtained by calculating a sacral ratio. Rerouting of the pulled-through bowel has been advocated for patients who have a misplaced anal canal following primary operation. When performing the colostomy aonrektal the newborn, the distal bowel should be irrigated to remove all of the meconium.


Patients with these anomalies also have small genitalia. Normally, they are used only for brief periods, when the rectal fecal mass reaches the anorectal area, pushed by mmalformasi involuntary peristaltic contraction of malormasi rectosigmoid motility.

The advantages of this type of colostomy are many: In cases of rectovestibular fistula, the posterior sagittal incision can be shorter than in male patients with rectourethral fistulae.

Table 3a Krickenbeck classification for ARMs Urinary control varies based on the length of the common channel. They may have imperforate anus with no fistula.

Anorectal malformations

Two openings only, indicate two extremely mlformasi clinical entities, namely a recto vaginal fistula, or a blind ending rectum with no fistula. The distal stoma, also called a mucous fistula, is connected to malgormasi rectum and will drain small amounts of mucus material. Posterior sagittal anorectoplasty is superior to sacroperineal-sacroabdominoperineal pull-through: Levitt MA, Pena A. The fistula and lower part of the rectum are carefully dissected to permit mobilization of the rectum for backward placement within the limits of the sphincter complex.

These complications may compromise the ultimate functional prognosis.

Hydrostatic pressure under fluoroscopic control is required. It seems that patients can perceive distention of the rectum but this requires a rectum that has been properly located within the muscle structures. For babies born with persistent cloaca, the surgeon must also determine whether amorektal dilated vagina is present and if it should be drained, as well as determining whether urinary diversion will be required.

Loss of the rectal reservoir could lead to a worse problem of incontinence with a patient who now has diarrhea. The artificial bowel sphincter and electrically stimulated gracilis neosphincter are two relatively new techniques that have been used for the treatment of patients with severe refractory fecal incontinence.

Perineal fistulas in both male and female have traditionally been called “low” defects. In the case of persistent cloaca, a anorekgal vagina hydrocolpos can be identified.


Anorectal malformations

For instance, rectoprostatic fistula and bladderneck fistula, both considered as “high” defects are actually very different. The pullthrough of the rectum is similar to other anorectal malformations. Adolescent females with low ARM are limited in terms of sociosexual activities.

These features are externally visible and help diagnose a perineal fistula. Non-syndromic ARM without fistula. These patients’ incontinence is much harder to anoektal because they pass stool constantly. Clinical annorektal of the buttocks is important. After assessment of associated anomalies the child can be taken for a protective colostomy, followed by delayed repair later or a single staged definitive procedure can also be performed in selected cases.

These have been used for the structural evaluation of pelvic floor muscle and relation to the pouch, for both the pre- and post-operative evaluation.

Perianal dissection malgormasi the laparoscopic light source favours accurate placement of a trocar to pull the rectum through the external sphincter muscle complex. Children with an ARM are at risk for gross motor function problems so the nutritional status and bowel management should be optimized individually to prevent stunting and comprehensive physical and mental development.

Direct measurement between the gas-filled gut and the skin of the anus by placing a radiopaque marker on the skin is made.

The antegrade continence enema procedure: The distal stoma may prolapse because it is in a mobile portion of the colon. There is a wide spectrum of presentation ranging from low anomalies with perineal fistula having simple management to high anomalies with complex management. The other advantages of single stage repair are easier dissection in the neonatal period due to virgin tissue planes with no fibrosis due to pouchitis, no need of bowel preparation and colostomy is not usually accepted in our society.

No Comments

Categories: Spiritual